A simple novel appliance for prosthodontic rehabilitation of a child with hypohidrotic ectodermal dysplasia – A case report

• Author Details:   
• Shweta Kajjari ^*
• Krishna Kadam
• Vidyavathi H. Patil
• Chaitanya Uppin
• Chandrashekhar Badakar
• Bhuvanesh Bhusari

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A particular condition known as Ectodermal Dysplasia (ED) is defined by the congenital abnormality of one or more ectodermal components. Symptoms include abnormalities in the skin, nails and sweat glands. Many dental abnormalities, such as hypodontia, anodontia, impacted teeth, and peg-shaped or conical front teeth, inadequate alveolar ridge development are among the oral features. These diseases affect 1 in 10,000 to 1 in 100,000 newborns, which is a relatively low incidence. Clinically, ED can be categorised as Christ Siemens-Touraine syndrome, which is anhidrotic or hypohidrotic X-linked type that is inherited, characterised by the typical triad of hypodontia, hypohidrosis, and hypotrichosis, as well as by facial dysmorphism and other one is Hidrotic (Syndrome de Louis).Hidrotic kind of ED, which is inherited as an autosomal characteristic, can damage the teeth, hair, and nails but often spares the sweat glands. In ED patients, prosthetic dental therapy aims to retain alveolar ridges, promote early perioral musculature development, improve speech, and restore normal face features. This promotes typical emotional and psychological growth. In present case report, the aetiology, clinical symptoms, therapeutic possibilities of this hereditary illness and prosthetic management of oligontia are described and discussed.

 Keywords:  Anhidrotic, Ectodermal Dysplasia, Hidrotic, Hypodontia.